Hemostasis Surgery of Spontaneous Hemothorax Complicating Neurofibromatosis Type 1

Author Info

Abdennadher Mahdi Ben Saad Soumaya Zribi Hazem Zairi Sarra Bouassida Imen Marghli Adel

Corresponding Author

Abdennadher Mahdi
El-Manar University, Tunisia

A B S T R A C T

Vascular lesions in Von Recklinghausen’s disease also known as Neurofibromatosis type 1 (NF1), are rare but have a fatal and potentially life threatening complications such as spontaneous hemothorax. An emergent thoracotomy is indicated when there is an active bleeding associated unstable hemodynamic status. Despites surgery is laborious and unpredictable but it have a merit to stop hemorrhage. A conservative management with endovascular embolization or non-operative approach have also been reported in case of hemodynamic stability. We report two case report of spontaneous hemothorax in patient with Recklinghausen disease. A chest tube was immediately inserted for two patients. Due to continuous bleeding and hemodynamic instability (Patient 1), and the increase of pleural effusion volume (Patients 1 & 2), emergent surgery of thorax was done with favourable post-operative follow up.

Article Info

Article Type

Case Report

Publication history

Received: Tue 22, Dec 2020
Accepted: Mon 01, Feb 2021
Published: Fri 19, Feb 2021

Copyright

© 2023 Abdennadher Mahdi. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.CRSS.2021.01.01