Large Orbital Tumor in a Patient with Neurofibromatosis Type 2

Large Orbital Tumor in a Patient with Neurofibromatosis Type 2

Author Info

Corresponding Author
Taoufik Abdellaoui
Department of Ophthalmology, Military Teaching Hospital Med-V, Rabat, Morocco

A B S T R A C T

Neurofibromatosis type 2 (NF2) is a separate entity from Neurofibromatosis type 1 (NF1) or von Recklinghausen’s disease, and is much less frequent than NF1. Vestibular schwannomas are the hallmark lesion, affecting 95% of individuals and typically occur bilaterally. Schwannomas commonly occur on other nerves intracranially and in the spinal compartment, along with meningiomas, ependymomas, and gliomas. Ophthalmologic abnormalities are present in the majority of NF2 patients, including cataracts, retinal changes, optic nerve sheath meningiomas and other optic pathway tumors. These tumors are sometimes large and can induce significant proptosis. We report the case of a large orbital meningioma responsible for severe proptosis in a patient with NF2.

Article Info

Article Type
Case Report
Publication history
Received: Fri 17, Jul 2020
Accepted: Tue 04, Aug 2020
Published: Mon 24, Aug 2020
Copyright
© 2019 Taoufik Abdellaoui. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository. All rights reserved.
DOI: 10.31487/j.AJSCR.2020.03.11