Andrea Di  Bernardo,Fabio  Sciancalepore,Fabio L.  Giardina,M. Silvia  Spinelli,Matteo G.  Lo Duca,Primo A.  Daolio,Stefano  Bastoni,
Angiosarcoma Secondary to a Paget’s Disease: A Rare Clinical Case With 5 Years of Follow-Up and Review of the Literature
Case Reports and Series in Surgery
2020
2733-2241
http://dx.doi.org/10.31487/j.CRSS.2020.02.01
https://www.sciencerepository.org/angiosarcoma-secondary-to-a-paget-s-disease-a-rare-clinical-case_CRSS-2020-2-101 
Abstract: Paget's disease is characterized by disorganized bony tissue due to altered equilibrium of bone formation
and resorption. Its malignant transformation is well known and is usually described to an osteosarcoma,
often with bad prognosis. In this paper, we present a case clinic of an angiosarcoma from a Paget’s disease
of a pelvic bone. The patient underwent a surgical procedure of tumor resection with wide margins
(Enneking zone 2-3). The follow-up of 5 years in this case is unique in the literature.Keywords: Paget’s disease, Angiosarcoma, Pelvic resection, Paget’s sarcomatous transformation