TY - JOUR
AR - SCR-2019-2-104
TI - Extra-lobar Pulmonary Sequestration with Associated Asymptomatic Congenital Diaphragmatic Hernia
AU - Ira N., Adler
AU - Lilly , Bayouth
AU - Megan, Sippey
AU - Shannon , Longshore
JO - Surgical Case Reports
PY - 2019
DA - Wed 20, Mar 2019
SN - 2613-5965
DO - http://dx.doi.org/10.31487/j.SCR.2019.02.004
UR - https://www.sciencerepository.org/extra-lobar-pulmonary-sequestration-with-associated-asymptomatic-congenital-diaphragmatic-hernia_SR-SCR-2019-2-104 
KW - Pulmonary sequestration, congenital diaphragmatic hernia, bronchopulmonary foregut malformation
AB - Background
Pulmonary sequestration is a rare aberrant formation of non-functional pulmonary tissue that does not
communicate with the tracheobronchial tree or pulmonary blood supply. It can be associated with congenital
diaphragmatic hernias (CDH) which typically present in the newborn as respiratory distress and feeding
difficulties.
Case Presentation
A full term infant presents with an asymptotic left sided CDH with associated supra-diaphragmatic extralobar pulmonary sequestration intermittently sliding through the diaphragm. Prenatal imaging raised
suspicion for CDH; however, postnatal imaging in an asymptomatic infant confirmed suspected
sequestration and suggested intact diaphragm. The infant was taken to the operating room for elective
resection of the suspected supra-diaphragmatic sequestration. Intraoperative findings demonstrated a supradiaphragmatic extra-lobar pulmonary sequestration obscuring the undiagnosed CDH.
Conclusions
This rare presentation of a supra diaphragmatic pulmonary sequestration intermittently herniating through
an unrecognized asymptomatic CDH emphasizes the potential for unexpected intra-operative findings of
bronchopulmonary foregut malformation with associated CDH despite prior radiographic imaging results.