article = {SCR-2019-1-108}
title = {Infected Abdominal Cystic Lymphangioma: A Rare Cause of Inflammatory Acute Abdom}
journal = {Surgical Case Reports}
year = {2019}
issn = {2613-5965}
doi = {http://dx.doi.org/10.31487/j.SCR.2019.01.008}
url = {https://www.sciencerepository.org/infected-abdominal-cystic-lymphangioma-a-rare-cause-of-inflammatory-acute-abdomen_SR-SCR-2019-1-108 
author = {Angélica Maria Lucchese,Antonio Nocchi  Kalil,Fernanda  Onofrio ,Rodrigo Zanatta  Ribeiro,}
keywords = {cystic lymphangioma, infected retroperitoneal cyst, acute abdomen}
abstract ={Background: Cystic lymphangioma (CL) results from congenital malformation of the lymphatic channels
found especially in children, being rarely diagnosed in adults. Intra-abdominal location is unusual, and only
exceptionally may the abdominal cavity be infected.
Case report: We report the case of a 28-year-old man with retroperitoneal CL who presented with acute
abdominal pain, fever, signs of sudden decompression, and leukocytosis. Imaging studies showed an intraabdominal collection of fat density within the cyst. Presence of fat within an intra-abdominal cystic mass is
suggestive of a dermoid cyst (mature cystic teratoma), CL, or lymphocele. At laparotomy, the tumor was
found in the retroperitoneum and completely resected. Histopathology of the cystic lesion identified a
fibrinopurulent exudate and lymphatic channels interspersed with lymphoid stroma, while
immunohistochemistry showed positive staining for D2-40 and CD34, confirming the diagnosis of infected
retroperitoneal cyst.
Conclusions: Presentation as an acute abdomen is uncommon and surgery is the treatment of choice for
symptomatic patients with CL. The prognosis is excellent, and recurrence rates are extremely low if the cyst
is completely excised.}