Table 1: Case reports.



Age

Sex

Predisposing factors

Signs & Symptoms

Delay

Location

Histology

Dukes stage

Survival

1

11y10m

M

Ulcerative colitis

Ulcerative colitis

Colonoscopy control

Sigmoid- Rectum

Mucinous

D

alive

2

15y4m

M

-

Gastrointestinal bleeding

 + weight loss

3m

Sigmoid- Rectum

Mucinous + Signet-ring cells

C

Dead (OS 19.9m)

3

15y7m

F

-

Diarrhea + weight loss

2m

Hepato-colic angle

Mucinous

D

Dead (OS 6.2m)

4

13y11m

M

NF1 -High grade glioma

Abdominal pain + gastrointestinal bleeding

1.5m

Sigmoid

Mucinous

D

Dead

5

14y10m

M

-

-

-

Colon

Mucinous + Signet-ring cells

D

Dead (OS 11.3m)

6

15y5m

M

-

Abdominal pain + rectal bleeding + diarrhea + weight loss

4m

Rectum

Mucinous

-

Dead (OS 5.3m)

7

14y7m

F

-

Abdominal pain + anemia + weight loss

5m

Sigmoid- Rectum

Poorly differentiated

D

Dead (OS 7.9m)

8

19y

M

High grade glioma / glioblastoma

Lower gastrointestinal bleeding

-

-

 

-

-

Dead

9

17y

F

Crohn's disease

Crohn's disease

Colonoscopy control

Rectum

Well -differentiated

A

Dead (OS 10.3m)

10

16y

F

-

Acute surgical abdomen (occlusion) + anemia

8d

Hepatic flexure

Moderately differentiated

C

Dead (OS 18.5m)

11

14y9m

F

-

Acute surgical abdomen (pain + vomiting)

11d

Cecum

Signet-ring cells

D

Dead (OS 5.8m)

12

11y9m

M

-

Abdominal pain + change in bowel habits

3m

Sigmoid

Mucinous + Signet-ring cells

-

Dead

13

12y3m

M

-

Acute surgical abdomen + abdominal pain

3 m

Sigmoid

Signet-ring cells

-

Dead (OS 1.7m)

14

14y8m

M

-

Abdominal pain + weight loss + intestinal obstruction

3 m

Transverse

Mucinous

C

Dead

15

14y

M

-

Abdominal pain + vomiting + change in bowel habits

1m

Hepatic flexure

Moderately differentiated

C

Alive

y: Years; m: Months; d: Days; M: Male; F: Female; NF1: Neurofibromatosis type 1; OS: Overall Survival.