Table 1: Overall summary of the pooled studies.

Author

Year

Strategy

N pts

Early deaths

Total deaths

FU median (months)

Complete repair, N (%)

Age at repair median (days)

Pts with at least one reintervention

𝚫 Nakata

Postrepair RV/LV

Hofferberth et al.

2018

1

41

2

6

58

22 (54)

584

41

-

0.65

 

 

3

43

4

9

68

15 (35)

621

43

-

0.82

Rabinowitz et al.

2017

2

10

0

0

34

10 (100)

239

10

130

<0.5

Trezzi et al.

2017

1

95

8

21

102

64 (67)

365

11

 

0.49

Lenoir et al.

2017

2

109

3

10

60

84 (77)

252

29

173

<0.5

Bauser-Heaton et al.

2017

1

186

5

18

28

186 (100)

162

-

-

0.35

 

 

2

46

2

4

37

35 (76)

247

-

-

0.38

 

 

3

59

4

6

31

39 (66)

367

-

-

0.39

Soquet et al.

2016

1

4

0

0

55

4 (100)

258

1

-

-

 

 

2

33

0

3

54

22 (67)

617

13

-

0.64

Ikeda et al.

2015

3

13

1

2

13

9 (69)

540

-

-

0.44

Kim et al.

2015

2

15

0

2

70

13 (87)

582

3

163.2

0.57

Watanabe et al.

2014

1

27

0

2

48

27 (100)

34

8

-

0.35

Gerelli et al.

2014

2

57

2

12

36

47 (82)

10

26

121

-

Fang et al.

2014

2

103

0

0

11

66 (64)

-

-

61

-

Hibino et al.

2013

2

23

0

3

44.7

20 (87)

-

17

225

 

Mainwaring et al.

2012

2

35

0

29

49

18 (51)

-

35

-

0.39

Liava et al.

2012

2

20

0

0

39

12 (60)

570

17

86.9

0.64

Dragulescu et al.

2011

2

20

1

4

98.4

19 (95)

744

19

182

0.58

Mei et al.

2010

3

11

1

1

24

10 (91)

-

0

-

-

Murthy et al.

2010

1

124

16

19

72

74 (60)

1152

-

-

0.66

Honjo et al.

2009

1

20

0

1

31

19 (95)

234

10

-

-

Song et al.

2009

3

40

2

7

54.5

17 (43)

1080

4

115

0.57

Brizard et al.

2009

2

15

0

0

-

7 (47)

600

-

-

0.59

Mumtaz et al.

2008

2

40

2

4

68

25 (63)

-

13

149.3

-

Ishibashi et al.

2007

1

113

6

26

105.6

91 (81)

243

-

-

0.7

Amark et al.

2006

1

57

-

26

45

57 (100)

720

94

102

0.5

 

 

3

128

-

28

45

82 (64)

720

-

74

-

D’Udekem et al.

2005

3

82

7

16

170.4

53 (65)

1440

18

-

0.62

Griselli et al.

2004

1

37

1

4

144

37 (100)

-

41

-

0.6

 

 

3

119

14

22

-

89 (75)

-

-

-

-

Duncan et al.

2003

3

46

0

1

44

28 (61)

1050

14

-

0.45

Gupta et al.

2003

3

104

12

17

122

58 (56)

1872

19

-

0.5

Rodefeld et al.

2002

2

18

0

2

-

11 (61)

138

-

-

-

Pooled

 

 

1893

93

305

48

1370 (72)

570

475

121

0.54