Surgical Treatment of Abdominal Aortic Aneurysm in a 3-Year-Old Girl with Tuberous Sclerosis Complex

Surgical Treatment of Abdominal Aortic Aneurysm in a 3-Year-Old Girl with Tuberous Sclerosis Complex

Author Info

Corresponding Author
José I. Aramendi
Division of Cardiac Surgery, Cruces University Hospital, Barakaldo, Spain

A B S T R A C T

The tuberous sclerosis complex is a multisystem disorder affecting children and adults. The association between abdominal aortic aneurysm and tuberous sclerosis is rare. We present 3-year-old girl with a pulsatile abdominal mass in the pediatrician´s medical review. An abdominal evaluation showed a 6cm infrarenal abdominal aortic aneurysm. The patient underwent open repair with a 14-mm Dacron tube graft. The histological examination revealed connective tissue proliferation, fibrosis, and calcification of the aortic wall. Frequent follow-ups with ultrasounds showed no alterations. Due to the high risk of rupture, early surgical repair is the first-line therapy.

Article Info

Article Type
Case Report
Publication history
Received: Mon 27, Jul 2020
Accepted: Fri 07, Aug 2020
Published: Sat 15, Aug 2020
Copyright
© 2023 José I. Aramendi. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.SCR.2020.08.19