Extra-lobar Pulmonary Sequestration with Associated Asymptomatic Congenital Diaphragmatic Hernia

Extra-lobar Pulmonary Sequestration with Associated Asymptomatic Congenital Diaphragmatic Hernia

Author Info

Corresponding Author
Lilly Bayouth
Department of Surgery, Brody School of Medicine at East Carolina University, 600 Moye Blvd, Greenville, NC, 27834, USA

A B S T R A C T

Background Pulmonary sequestration is a rare aberrant formation of non-functional pulmonary tissue that does not communicate with the tracheobronchial tree or pulmonary blood supply. It can be associated with congenital diaphragmatic hernias (CDH) which typically present in the newborn as respiratory distress and feeding difficulties. Case Presentation A full term infant presents with an asymptotic left sided CDH with associated supra-diaphragmatic extralobar pulmonary sequestration intermittently sliding through the diaphragm. Prenatal imaging raised suspicion for CDH; however, postnatal imaging in an asymptomatic infant confirmed suspected sequestration and suggested intact diaphragm. The infant was taken to the operating room for elective resection of the suspected supra-diaphragmatic sequestration. Intraoperative findings demonstrated a supradiaphragmatic extra-lobar pulmonary sequestration obscuring the undiagnosed CDH. Conclusions This rare presentation of a supra diaphragmatic pulmonary sequestration intermittently herniating through an unrecognized asymptomatic CDH emphasizes the potential for unexpected intra-operative findings of bronchopulmonary foregut malformation with associated CDH despite prior radiographic imaging results.

Article Info

Article Type
Case Report
Publication history
Received: Thu 15, Feb 2018
Accepted: Tue 05, Mar 2019
Published: Wed 20, Mar 2019
Copyright
© 2023 Lilly Bayouth. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.SCR.2019.02.004